Clinical and EEG-EMG characteristics of perioral myoclonia with absence seizures

Perioral myoclonia with absence (POMA) epilepsy was first reported by Panayiotopoulos et al. in 1994 [1], and has not yet been classified as a separate seizure type or epilepsy syndrome by the International League Against Epilepsy (ILAE) [2–5]. The main clinical characteristic of POMA is perioral myoclonia, which consists of rhythmic contractions of the orbicularis oris muscle, causing protrusion of the lips; contractions of the depressor anguli oris muscle, resulting in twitching at the corners of the mouth; and, rarely, more widespread involvement, including the muscles of mastication, producing jerking movements of the jaw.

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