Brugada syndrome is a rare inherited channelopathy predisposing to ventricular arrhythmias and leading to an increased risk of sudden cardiac death, despite a structurally normal heart. The most common mutation is a loss-of-function mutation in SCN5A gene, rsesponsible for encoding the α-subunit of the sodium channel. Diagnosis is based on a specific electrocardiogram (ECG) pattern, observed either spontaneously or during a sodium channel blocker test. Considering the two different Brugada pattern types, type 1 is the most frequently associated with the SCN5A gene mutation [1].
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