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Dravet syndrome (DS) is an infantile-onset developmental and epileptic encephalopathy characterized by febrile seizures in the first year of life, followed by the appearance of afebrile seizures of varying semiologies which are almost always drug-resistant.1 Approximately 80-90% of patients have SCN1A pathogenic variants.2 EEG is typically normal at the time of first presentation, but various abnormalities may be seen later, including generalized or focal slowing, generalized spike-wave, and focal or multifocal spikes or spike-wave discharges.