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Dravet Syndrome (DS), previously known as “severe myoclonic epilepsy of infancy (SMEI)”, was first described by Charlotte Dravet in 1978. [1] DS is a rare, early-onset, treatment-resistant, epileptic encephalopathy that presents in the first or second year of life [2]. The reported incidence is between 1 in 15,000 to 1 in 41,000 [3–5]. In the late 1980s and early 1990s, variability was noticed amongst the myoclonic seizures, where they were absent in some patients. These patients were classified as having borderline SMEI, known as SMEIB.