Epilepsy with myoclonic-atonic seizures (EMAS), previously known as epilepsy with myoclonic astatic seizures, or Doose syndrome, is a syndrome characterized by the presence of myoclonic-atonic seizures in an otherwise normal child who may have a history of febrile and/or afebrile generalized seizures (generalized, myoclonic, atypical absence, and tonic seizures) [1–8]. EMAS is now considered to be a developmental and epileptic encephalopathy. Non-convulsive status epilepticus (NCSE) is seen in 17–40 % [1,5], with longer duration NCSE correlating with a poorer prognosis [1,6].
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