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Dravet syndrome (DS), otherwise known as severe myoclonic epilepsy of infancy (SMEI), is a severe and rare drug-resistant seizure disorder with an incidence of 1 in 20,000 to 1 in 40,000 [1–2]. Between 70% and 80% of patients with DS carry sodium channel α1 subunit gene (SCN1A) abnormalities [3]. The characteristics of DS include early onset (before 1 year of age). Infants with DS often present with prolonged, hemiconvulsive seizures triggered by fever; other seizure types, including focal with impaired awareness, absence, and myoclonic seizures, develop between 1 and 4 years.