Hypothalamic hamartomas (HH) are rare (1:200000) congenital heterotopic and non-neoplastic lesions [1]. They can be attached to the hypothalamus at the inferior part of the third ventricle or to its wall, to the tuber cinereum, or to the mammillary bodies. HH are composed of mixed neuronal and glial cells that usually take the form of nodules. They can be isolated or associated with other brain lesions, or be part of a genetic syndrome, especially Pallister-Hall syndrome. The usual clinical presentation is drug-resistant gelastic or dacrystic seizures starting during the first year of life, and/or endocrinological disturbance such as precocious puberty.
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DIC
DIC
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